“ An X-linked disease (therefore only males are affected) due to a deficiency of either factor 8 or 9. Haemophilia arthopathy arises from ...
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An X-linked disease (therefore only males are affected) due to a deficiency of either factor 8 or 9. Haemophilia arthopathy arises from repeated bleeds, leading to the formation of pannus that erodes cartilage and leads to loss of subchondral bone and subarticular cyst formation. Intra-articular haemorrhage causes a chronic synovitis, synovial proliferation and periarticular osteopenia. Typically presents in affected patients aged 10-20 years with a tense, warm joint, fever and leucocytosis.
PLAIN FILM
• Accelerated maturation and enlargement of the epiphysis
• Soft tissue swelling
• Juxta-articular osteoporosis
• Erosion of the articular surface with subchondral cysts
• Preservation of joint space
• Squared patella with widening of the intercondylar notch
• Medial slanting of the tibiotalar joint and flattening of the condylar surface
MRI
• Low signal returned from hypertrophied synovium due to magnetic susceptibility of haemosiderin.
• Articular surfaces are devoid of cartilage.
• Joint effusion.
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