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Monostotic fibrous dysplasia

“ Accounts for up to 80% of fibrous dysplasia, it presents at between 5 and 15 years of age (75% by <30 years of age). It presents with p...

Accounts for up to 80% of fibrous dysplasia, it presents at between 5 and 15 years of age (75% by <30 years of age). It presents with pain or pathological fracture and rarely becomes malignant (<1%).
FEATURES
•  Most commonly affects the ribs (most common benign rib tumour).
 Femur (proximal most), tibia and craniofacial bones are next most common.
•  Commonly affects the proximal femur, then distal femur.
•  Craniofacial fibrous dysplasia may give the leontiasis ossea appearance 
•  Obliteration of the paranasal sinuses.
 Leontiasis ossea. Axial CT image of the facial bones demonstrating asymmetrical cortical thickening/ground-glass appearance of the right facial bones with obliteration/involvement of the sphenoid and ethmoid sinuses.